TY - JOUR
T1 - CONCURRENT IDIOPATHIC MACULAR TELANGIECTASIA TYPE 2 AND CENTRAL SEROUS CHORIORETINOPATHY
AU - Matet, Alexandre
AU - Yzer, Suzanne
AU - Chew, Emily Y
AU - Daruich, Alejandra
AU - Behar-Cohen, Francine
AU - Spaide, Richard F
PY - 2018/1
Y1 - 2018/1
N2 - PURPOSE: To describe cases presenting with features of idiopathic macular telangiectasia (MacTel) Type 2 and central serous chorioretinopathy (CSC).METHODS: Databases from four tertiary retina centers were searched for cases copresenting CSC and MacTel Type 2.RESULTS: Five cases were identified (4 men, 1 woman; mean age: 67.2 years). Four patients were referred for chronic or nonresolving CSC, and the diagnosis of MacTel Type 2 was made based on multimodal imaging findings. One patient had advanced MacTel Type 2, and developed acute CSC. Regarding the MacTel Type 2 findings, all subjects presented perifoveal telangiectasia on fluorescein angiography, and four subjects showed intraretinal cavitations typical of MacTel Type 2 on optical coherence tomography, in one or both eyes. Regarding the CSC findings, fluorescein angiography identified focal or extended retinal pigment epithelium alteration in all eyes, and an active leakage in two eyes. Indocyanine green angiography showed choroidal vascular hyperpermeability in four subjects. On optical coherence tomography, pigment epithelial detachments were detected in five eyes (four subjects), and foveal detachments were present in five eyes (three subjects), which spontaneously resolved (two eyes), responded to photodynamic therapy (two eyes), or persisted (one eye). Mean choroidal thickness was 402 ± 99 μm.CONCLUSION: The codiagnosis of CSC and MacTel Type 2 should be considered in atypical presentations associating features from both disorders.
AB - PURPOSE: To describe cases presenting with features of idiopathic macular telangiectasia (MacTel) Type 2 and central serous chorioretinopathy (CSC).METHODS: Databases from four tertiary retina centers were searched for cases copresenting CSC and MacTel Type 2.RESULTS: Five cases were identified (4 men, 1 woman; mean age: 67.2 years). Four patients were referred for chronic or nonresolving CSC, and the diagnosis of MacTel Type 2 was made based on multimodal imaging findings. One patient had advanced MacTel Type 2, and developed acute CSC. Regarding the MacTel Type 2 findings, all subjects presented perifoveal telangiectasia on fluorescein angiography, and four subjects showed intraretinal cavitations typical of MacTel Type 2 on optical coherence tomography, in one or both eyes. Regarding the CSC findings, fluorescein angiography identified focal or extended retinal pigment epithelium alteration in all eyes, and an active leakage in two eyes. Indocyanine green angiography showed choroidal vascular hyperpermeability in four subjects. On optical coherence tomography, pigment epithelial detachments were detected in five eyes (four subjects), and foveal detachments were present in five eyes (three subjects), which spontaneously resolved (two eyes), responded to photodynamic therapy (two eyes), or persisted (one eye). Mean choroidal thickness was 402 ± 99 μm.CONCLUSION: The codiagnosis of CSC and MacTel Type 2 should be considered in atypical presentations associating features from both disorders.
KW - Aged
KW - Central Serous Chorioretinopathy/complications
KW - Choroid/pathology
KW - Female
KW - Fluorescein Angiography/methods
KW - Follow-Up Studies
KW - Fundus Oculi
KW - Humans
KW - Macula Lutea/pathology
KW - Male
KW - Middle Aged
KW - Retina
KW - Retrospective Studies
KW - Telangiectasia, Hereditary Hemorrhagic/complications
KW - Tomography, Optical Coherence/methods
KW - Visual Acuity
U2 - 10.1097/IAE.0000000000001836
DO - 10.1097/IAE.0000000000001836
M3 - Article
C2 - 29016451
SN - 0275-004X
VL - 38 Suppl 1
SP - S67-S78
JO - Retina
JF - Retina
ER -